A Rare Differential Diagnosis for Acute Urticarial Plaques: Adult Onset Still’s Disease

Authors

  • Pırıl Etikan Akbaş Department of Dermatology and Venerology, Okmeydani Training and Research Hospital, Istanbul
  • Nilgün Bahçetepe Hökenek Department of Dermatology and Venerology, Okmeydani Training and Research Hospital, Istanbul
  • Mehmet Çopur Department of Dermatology and Venerology, Okmeydani Training and Research Hospital, Istanbul
  • Şule Güngör Department of Dermatology and Venerology, Okmeydani Training and Research Hospital, Istanbul
  • Duygu Temiz Karadağ Department of Internal Medicine, Kocaeli University Medical Faculty Hospital, Kocaeli
  • Ayşe Cefle Ergüney Department of Internal Medicine, Kocaeli University Medical Faculty Hospital, Kocaeli
  • Emek Kocatürk Department of Rheumatology, Kocaeli University Medical Faculty Hospital, Kocaeli

Keywords:

Adult-onset Still’s Disease, urticaria, cutaneous findings

Abstract

Adult-onset Still’s disease (AOSD) was first described by Bywaters as a different clinical entity from Juvenile Rheumatoid Arthritis (Still’s Disease). It is an uncommon, acute, systemic inflammatory disease of unknown etiology, which is characterized by a high spiking fever (≥39°C), typical skin rash with an evanescent salmon-pink erythema, leukocytosis, arthritis/arthralgia, hepatosplenomegaly, lymphadenopathy, leukocytosis, sore throat and serositis. We report two patients in whom urticaria-like rash and angioedema were uncommon presenting features of AOSD where treatment was attempted with antihistamines and systemic steroids. AOSD should be kept in mind in persistent urticarial skin rash with accompanying spiking fever.

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Published

2018-01-03

How to Cite

1.
Etikan Akbaş P, Bahçetepe Hökenek N, Çopur M, Güngör Şule, Temiz Karadağ D, Cefle Ergüney A, Kocatürk E. A Rare Differential Diagnosis for Acute Urticarial Plaques: Adult Onset Still’s Disease. AAI [Internet]. 2018 Jan. 3 [cited 2022 Jan. 24];15(3):152-7. Available from: https://aai.org.tr/index.php/aai/article/view/47

Issue

Section

Case Reports