Objective: The aim of study is to determine the clinical features of our patients with primary immunodeficiency in a region of eastern Turkey.

Materials and Methods: The medical records with primary immunodefi ciency (PID) who were followed ornewly diagnosed in Ataturk University School of Medicine and Erzurum Regional Training and Research Hospital Department of Pediatric Immunology and Allergy between June 2013 and June 2015 were evaluated retrospectively.

Results: Totally 100 patients were followed in our center. Antibody defi ciency was seen in 80% of patients while other immunodefi ciencies were phagocytic system defects in 6%, severe combined immunodefi ciency in 5%, immun disregulation defects in 4%, innate immun system defects in 2%, other defects in 3%.

Discussion: Other than the patients living in Erzurum, the patients from the Eastern Anatolia Region are also usually admitting to Erzurum hospitals. Wethink that the PID patients in this region are more than our known patients. So we think that the doctors, who care with pediatric population, should be educated for PID patients.